The final diagnosis is based on the genetic analysis of LAMP2 gene.
  There are no diagnostic ECG findings. Nonspecific ECG abnormalities are frequently seen.
ECG findings in Danon disease
  Wolff-Parkinson-White (WPW) pattern (68% of male, 27% of female patients) (common). WPW pattern is NOT due to an accessory pathway. Seemingly delta wave is in fact due to slurring of the initial part of QRS complex.
ECG 1. The ECG above belongs to a 21 years-old male with Danon disease.
WPW pattern (short PR interval, slurred upstroke of the QRS complex mimicking delta wave),
increased QRS voltage (left ventricular hypertrophy pattern) and extensive T wave negativity are seen.
Drs. Torsten Konrad and Thomas Rostock have donated the above ECG to our website.